Auditory Brainstem Implant in Prelingually Deaf Children

Introduction: Auditory brainstem implant (ABI) has been placed in children who are born deaf due to cochlear nerve aplasia or with a severe degree of inner ear dysplasia, and for whom a cochlear implant is not an option. Application of ABI is more complicated than cochlear implant because ABI electrodes...

Audiologic findings in children with biotinidase deficiency in Turkey

Biotinidase deficiency is an autosomal recessively inherited disorder characterized by neurological and cutaneous features, including sensorineural hearing loss. Although many features of the disorder are reversible following treatment with biotin, the hearing loss appears to be irreversible. In the present study, hearing status of patients with biotinidase deficiency is characterized...